Visualize Submit Comment
Metadata
ID DOID:12132
Name granulomatosis with polyangiitis
Definition An autoimmune disease that is characterized by necrotizing granulomatous inflammation of the upper and lower respiratory tract, glomerulonephritis, vasculitis, and the presence of antineutrophil cytoplasmatic autoantibodies (ANCAs) in patient sera, and is located_in lung, located_in kidney, located_in skin resulting from an autoimmune attack by antineutrophil cytoplasmic antibodies against small and medium-size blood vessels.
https://en.wikipedia.org/wiki/Granulomatosis_with_polyangiitis
Xrefs

GARD:7880

ICD10CM:M31.3

ICD9CM:446.4

MESH:D014890

NCI:C3444

OMIM:608710

SNOMEDCT_US_2023_03_01:195353004

UMLS_CUI:C3495801

Subsets

DO_rare_slim

NCIthesaurus

Synonyms

Necrotizing respiratory granulomatosis [EXACT]

Wegener granulomatosis, formerly [EXACT]

Parent Relationships

is_a lung disease

is_a kidney disease

is_a skin disease

is_a autoimmune disease of blood

Add an item to the term tracker